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KMID : 0367419960390081151
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Journal of Korean Pediatric Society
1996 Volume.39 No. 8 p.1151 ~ p.1157
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A Case of Intestinal Neuronal Dysplasia
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김세영
최연호/서정기/김종재/김인원
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Abstract
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Intestinal neuronal dysplasia(IND) is a disease characterized clinically by symptoms of intestinal obstruction and pathologically by hyperplasia of the submucosal and myenteric plexuses with formation of giant ganglia. Chronic intestinal
pseudo-obstruction is a clinical diagnosis, composed of myopathic form and neuropathic form, and normal intestinal histology. Intestinal neuronal dysplasia is a neuropathic form of chronic intestinal pseudo-obstruction. The clinical presentation
and the
course of IND is very variable.
We experienced a case of intestinal neuronal dysplasia in a 5 year-old boy who had suffered from recurrent abdominal pain and vomiting for 3 years. Small bowel series showed multiple intestinal dilatations and delayed excretion of contrast media.
He
underwent exploratory laparotomy. However no mechanical causes for markedly dilated intestine were found and he received loop ileostomy. However, he suffered from recurrent vomiting and abdominal pain. So, he received repair-operaton. The
pathology
of
surgical specimen showed hyperplasia of the submucosal and myenteric plexuses with giant ganglia. We report this cases with a brief review of the related literatures.
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KEYWORD
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